Shone Syndrome Life Expectancy

Shone et al 1963. Patients with Shones syndrome have a poor long-term prognosis with a perioperative mortality rate of 2427 often requiring multiple interventions at an early age. The long-term prognosis for patients with Shones Complex depends on the extent of mitral valve disease the degree to which the left ventricle is hypoplastic or abnormally small and the cumulative effects of surgical treatments. The Adult with Shones Complex 2014 Download Printable Version. Patients with Shones syndrome have been described as having an unsatisfactory operative outcome with a mortality rate of 2427 they require multiple interventions and have poor long-term prognosis 2-4. Complete and incomplete Shones syndrome. Eur J Echocardiogr 9.

Shone et al 1963.

Supra-valvar mitral ring or membrane parachute mitral valve sub-aortic membrane and coarctation of the aorta. Shone complex is an under-recognized entity associated with relatively low mortality in adulthood but substantial morbidity related to arrhythmias heart failure and interventions. Brauner RA Laks H Drinkwater DC Jr Scholl F McCaffery S 1997 Multiple left heart obstructions Shones anomaly with mitral valve involvement. Shone Syndrome A rare congenital heart disease described by Shone in 1963 Manifests as decreased left ventricular output There are two types of Shones syndrome. Fewer than 50 cases of Shones syndrome have been reported in the literature and most of them focus on postnatal surgical outcome with. Our patient is unique due to his prolonged survival which allowed the opportu-.

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Shone syndrome life expectancy. A supravalve mitral membrane SVMM parachute mitral valve subaortic stenosis membranous or muscular and coarctation of the aorta. Our patient is unique due to his prolonged survival which allowed the opportu-. 6 9 Patients with Shone syndrome have a poor long-term prognosis and often require multiple interventions in the early months of life.

Since most patients with this syndrome are diagnosed during infancy or childhood and have a short life expec- tancy we do not have enough information about the natur- al history of long-standing disease. Increased awareness of this condition and associated complications may allow for more tailored follow-up. Heather Williams RCCS RDCS PE Shones complex is a rare congenital heart defect consisting of multiple left-sided obstructive heart lesions including.

Supra-valvar mitral ring or membrane parachute mitral valve sub-aortic membrane and coarctation of the aorta. The survivors have been followed from 1 to 16 years mean follow-up 6 - 1 years. Eur J Echocardiogr 9.

Shone complex is an under-recognized entity associated with relatively low mortality in adulthood but substantial morbidity related to arrhythmias heart failure and interventions. There were no late or sudden deaths. 4 5 In their first description of the syndrome Shone et al.

Symptoms of congestive heart failure which can occur in the first week of life include fatigue rapid breathing and wheezing faster than normal heart rate poor oral intake poor weight gain fluid retention edema in the legs pallor anemia and frequent pneumonias. The long-term prognosis for patients with Shones Complex depends on the extent of mitral valve disease the degree to which the left ventricle is hypoplastic or abnormally small and the cumulative effects of surgical treatments. Patients with Shones syndrome have been described as having an unsatisfactory operative outcome with a mortality rate of 2427 they require multiple interventions and have poor long-term prognosis 2-4.

These affect blood flow to and from the left ventricle or lower left heart chamber. The Adult with Shones Complex 2014 Download Printable Version. Shone et al 1963.

What are the symptoms of Shones syndrome. Shone Syndrome A rare congenital heart disease described by Shone in 1963 Manifests as decreased left ventricular output There are two types of Shones syndrome.

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There were no late or sudden deaths.

Fewer than 50 cases of Shones syndrome have been reported in the literature and most of them focus on postnatal surgical outcome with. A supravalve mitral membrane SVMM parachute mitral valve subaortic stenosis membranous or muscular and coarctation of the aorta. The long-term prognosis for patients with Shones Complex depends on the extent of mitral valve disease the degree to which the left ventricle is hypoplastic or abnormally small and the cumulative effects of surgical treatments. Patients with Shones syndrome have a poor long-term prognosis with a perioperative mortality rate of 2427 often requiring multiple interventions at an early age. John Shone in 1953. Complete and incomplete Shones syndrome. Eur J Echocardiogr 9. Essentially it is both a left ventricular inflow and outflow obstruction. 4 5 In their first description of the syndrome Shone et al.

The Adult with Shones Complex 2014 Download Printable Version. Shone syndrome is a collection of eight left-sided obstructive heart lesions. The Adult with Shones Complex 2014 Download Printable Version. There were no late or sudden deaths. The long-term prognosis for patients with Shones Complex depends on the extent of mitral valve disease the degree to which the left ventricle is hypoplastic or abnormally small and the cumulative effects of surgical treatments. Shone syndrome was identified by Dr. Shone complex is an under-recognized entity associated with relatively low mortality in adulthood but substantial morbidity related to arrhythmias heart failure and interventions.